Orthodontic and Orthopedic Treatment of a Patient with Incontinentia Pigmenti    
Yazarlar (3)
Ercan Cenk Doruk
Cumhuriyet Üniversitesi, Türkiye
Hasan Babacan
Pamukkale Üniversitesi, Türkiye
Makale Türü Özgün Makale
Makale Alt Türü SSCI, AHCI, SCI, SCI-Exp dergilerinde yayınlanan tam makale
Dergi Adı ANGLE ORTHODONTIST
Dergi ISSN 0003-3219 Wos Dergi Scopus Dergi
Dergi Tarandığı Indeksler SSCI
Dergi Grubu Q4
Makale Dili İngilizce
Basım Tarihi 12-2003
Cilt No 73
Sayı 6
Sayfalar 763 / 768
Özet
Incontinentia pigmenti is an uncommon, inherited disorder with predominantly ectodermal manifestations that is associated with skin (100%)), dental (90%), skeletal (40%), central nervous (40%), and ocular (35%) deformities. It is an X-linked dominant disease, usually lethal in males and occurring in female infants. The dental effects include delayed eruption, partial anodontia, microdontia, and cone or peg-shaped teeth. The dental, clinical, and radiological findings in a 16-year-old female are presented here. The patient had peg-shaped teeth and a unilateral maxillary transverse discrepancy associated with oligodontia in the maxillary and mandibular arches. Orthodontic treatment included rapid maxillary expansion and fixed orthodontic therapy for prosthetic purposes and elimination of the functional midline shift.
Anahtar Kelimeler
incontinentia pigmenti | partial anodontia | rapid maxillary expansion
BM Sürdürülebilir Kalkınma Amaçları
Atıf Sayıları
WoS 8

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